ABSTRACT

Sjögren syndrome (SS) is a systemic autoimmune disease which is mainly characterized by the inflammation and dysfunction of exocrine glands, however, many organs might be involved. Kidney involvement is seen in 5-14% of patients. Our case was presented with hypokalemic paralysis and hyperchloremic normal anion gap metabolic acidosis. The findings were consistent with type 1 renal tubular acidosis (RTA). The patient was diagnosed with SS due to mouth and eye dryness, anti-nuclear antibody (ANA), anti-SSA, and anti-SSB positivity and minor salivary gland biopsy. The patient's clinical findings and metabolic acidosis were controlled by the addition of immunosuppressive treatment.