ABSTRACT

Adult Still's disease of unknown etiology and pathogenesis is an acute onset of systemic inflammatory disease. Fever, skin rash, musculoskeletal, reticuloendothelial, and rarely, cardiopulmonary involvement, are predominantly observed. Adult Still's disease generally presents with multiple chronic diseases. We aimed to present a 35-year-old woman, diagnosed with Adult Still's disease and started corticosteroids therapy. While quickly decreasing corticosteroids dosage due to complications, neutropenia was revealed in the follow-up. Further tests were done to determine the cause of neutropenia. The patient was defined as having Adult Still's disease accompanied by hemophagocytic syndrome.