Coexistence of gastrointestinal Behçet’s disease, myelodysplastic syndrome and trisomy 8: A case report
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Case Report
P: 134-136
December 2021

Coexistence of gastrointestinal Behçet’s disease, myelodysplastic syndrome and trisomy 8: A case report

J Turk Soc Rheumatol 2021;13(3):134-136
1. Eskişehir Osmangazi Üniversitesi Tıp Fakültesi, İç Hastalıkları Anabilim Dalı, Romatoloji Bilim Dalı, Eskişehir, Türkiye
2. Eskişehir Osmangazi Üniversitesi Tıp Fakültesi, İç Hastalıkları Anabilim Dalı, Hematoloji Bilim Dalı, Eskişehir, Türkiye
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Received Date: 19.02.2020
Accepted Date: 11.05.2020
Publish Date: 22.12.2021
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ABSTRACT

Behçet’s disease (BD) is a systemic vasculitis, while myelodysplastic syndrome (MDS) is a heterogeneous group of clonal hematologic disorders characterized by ineffective hematopoiesis. Some studies suggest a relationship between MDS and BD, especially intestinal BD, and trisomy 8 seems to play an important role in both diseases. The presence of trisomy 8 is thought to be related to the intestinal involvement of BD. Here, we presented a case with the coexistence of intestinal BD, MDS, and trisomy 8.

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